E88.49

E88.49: Other mitochondrial metabolism disorders

Billable / specific codeICD-10-CM

E88.49 is a billable, specific ICD-10-CM code for other mitochondrial metabolism disorders. It is valid for submission on a claim.

Check E88.49 with the rest of the claim: free scrubber

Excludes1 inherited from the categories above E88.49

A category’s note binds every code beneath it.

Written on E88.4: Mitochondrial metabolism disorders

disorders of pyruvate metabolism (E74.4)
Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.22)
Leigh's encephalopathy (G31.82)
Mitochondrial myopathy, NEC (G71.3)
Reye's syndrome (G93.7)

Written on E88: Other and unspecified metabolic disorders

histiocytosis X (chronic) (C96.6)

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

E88.49 is named in 1 Medicare coverage policy: 1 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

A57224Billing and Coding: Respiratory Care

Alphabetic index entries that lead here

MNGIE syndrome(Mitochondrial Neurogastrointestinal Encephalopathy)
NARP syndrome(Neuropathy, Ataxia and Retinitis pigmentosa)
Syndrome›Fukuhara
Syndrome›MNGIE(Mitochondrial Neurogastrointestinal Encephalopathy)
Syndrome›NARP(Neuropathy, Ataxia and Retinitis pigmentosa)
Disorder›metabolism NOS›mitochondrial›other specified

Code history

Unchanged in every release from FY2024 to FY2027.