E88.49 — Other mitochondrial metabolism disorders
E88.49 is a billable, specific ICD-10-CM code for other mitochondrial metabolism disorders. It is valid for submission on a claim.
Risk adjustment
E88.49 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.
Medicare coverage
E88.49 is named in 1 Medicare coverage policy — 1 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.
- A57224Billing and Coding: Respiratory Care
How E88.49 is indexed
Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E88.49.
- MNGIE syndrome(Mitochondrial Neurogastrointestinal Encephalopathy)
- NARP syndrome(Neuropathy, Ataxia and Retinitis pigmentosa)
- Syndrome›Fukuhara
- Syndrome›MNGIE(Mitochondrial Neurogastrointestinal Encephalopathy)
- Syndrome›NARP(Neuropathy, Ataxia and Retinitis pigmentosa)
- Disorder›metabolism NOS›mitochondrial›other specified
Related codes at this level
Codes that share E88.4. If E88.49 is not quite right, the correct code is usually one of these.
Questions about E88.49
- Is E88.49 a billable ICD-10-CM code?
- Yes. E88.49 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
- Where does E88.49 sit in the tabular list?
- Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).