H49.81

H49.81: Kearns-Sayre syndrome

Non-billable headerICD-10-CM

H49.81 is a non-billable header ICD-10-CM code for kearns-sayre syndrome. It cannot be billed on its own: choose one of the more specific child codes below.

Code also

Both codes may be needed to describe the encounter fully. Sequencing depends on the reason for the visit.

, if applicable, other manifestations, such as:
heart block (I45.9)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

Progressive external ophthalmoplegia with pigmentary retinopathy

Excludes2 inherited from the categories above H49.81

Not part of this code, but both may be coded when both are present.

Written on H49: Paralytic strabismus

internal ophthalmoplegia (H52.51-)
internuclear ophthalmoplegia (H51.2-)
progressive supranuclear ophthalmoplegia (G23.1)

Other codes that can never be billed with H49.81

Their own Excludes1 notes name this code, so the conflict is not listed above.

E88.4Mitochondrial metabolism disorders
G71.3Mitochondrial myopathy, not elsewhere classified
H49.4Progressive external ophthalmoplegia

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Code history

Unchanged in every release from FY2024 to FY2027.

Code to one of these instead H49.81

4 child codes. Green means billable.

Other codes under H49.8

H49.88Other paralytic strabismus