G71.3

G71.3: Mitochondrial myopathy, not elsewhere classified

Billable / specific codeICD-10-CM

G71.3 is a billable, specific ICD-10-CM code for mitochondrial myopathy, not elsewhere classified. It is valid for submission on a claim.

Check G71.3 with the rest of the claim: free scrubber

Excludes1: never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.21)
Leigh's encephalopathy (G31.82)
mitochondrial metabolism disorders (E88.4.-)
Reye's syndrome (G93.7)

Excludes2 inherited from the categories above G71.3

Not part of this code, but both may be coded when both are present.

Written on G71: Primary disorders of muscles

arthrogryposis multiplex congenita (Q74.3)
metabolic disorders (E70-E88)
myositis (M60.-)

Other codes that can never be billed with G71.3

Their own Excludes1 notes name this code, so the conflict is not listed above.

E88.4Mitochondrial metabolism disorders

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

G71.3 is named in 10 Medicare coverage policies: 10 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

A52494High Frequency Chest Wall Oscillation Devices - Policy Article
A52510Mechanical In-exsufflation Devices - Policy Article
A54095Billing and Coding: Nerve Conduction Studies and Electromyography
A54969Billing and Coding: Nerve Conduction Studies and Electromyography

Alphabetic index entries that lead here

Myopathy›mitochondrial NEC

Code history

Unchanged in every release from FY2024 to FY2027.