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E88.40

E88.40: Mitochondrial metabolism disorder, unspecified

Billable / specific codeICD-10-CM

E88.40 is a billable, specific ICD-10-CM code for mitochondrial metabolism disorder, unspecified. It is valid for submission on a claim.

Check E88.40 with the rest of the claim: free scrubber

Excludes1 inherited from the categories above E88.40

A category’s note binds every code beneath it.

Written on E88.4: Mitochondrial metabolism disorders

  • disorders of pyruvate metabolism (E74.4)
  • Kearns-Sayre syndrome (H49.81)
  • Leber's disease (H47.22)
  • Leigh's encephalopathy (G31.82)
  • Mitochondrial myopathy, NEC (G71.3)
  • Reye's syndrome (G93.7)

Written on E88: Other and unspecified metabolic disorders

  • histiocytosis X (chronic) (C96.6)

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Alphabetic index entries that lead here

  • Disorder›mitochondrial metabolism
  • Disorder›metabolism NOS›mitochondrial

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E88.4

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.