MCMCB Pro
E74.4

E74.4Disorders of pyruvate metabolism and gluconeogenesis

Billable / specific codeICD-10-CM

E74.4 is a billable, specific ICD-10-CM code for disorders of pyruvate metabolism and gluconeogenesis. It is valid for submission on a claim.

Excludes1 — never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • disorders of pyruvate metabolism and gluconeogenesis with anemia (D55.-)
  • Leigh's syndrome (G31.82)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Deficiency of phosphoenolpyruvate carboxykinase
  • Deficiency of pyruvate carboxylase
  • Deficiency of pyruvate dehydrogenase

Other codes that can never be billed with E74.4

These codes carry an Excludes1 note pointing at E74.4. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E74.4 alone.

  • E88.4Mitochondrial metabolism disorders

Risk adjustment

E74.4 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

E74.4 is named in 1 Medicare coverage policy 1 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography

How E74.4 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E74.4.

  • Deficiency, deficientphosphoenolpyruvate carboxykinase
  • Disordergluconeogenesis
  • Disorderpyruvate metabolism
  • Deficiency, deficientpyruvatecarboxylase
  • Deficiency, deficientpyruvatedehydrogenase
  • Disordermetabolism NOSpyruvate

Related codes at this level

Codes that share E74. If E74.4 is not quite right, the correct code is usually one of these.

Questions about E74.4

Is E74.4 a billable ICD-10-CM code?
Yes. E74.4 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E74.4 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
What cannot be coded together with E74.4?
E74.4 carries an Excludes1 note, which means the conditions it lists can never be coded together with it on the same encounter.
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.