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E76.3

E76.3Mucopolysaccharidosis, unspecified

Billable / specific codeICD-10-CM

E76.3 is a billable, specific ICD-10-CM code for mucopolysaccharidosis, unspecified. It is valid for submission on a claim.

Other codes that can never be billed with E76.3

These codes carry an Excludes1 note pointing at E76.3. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E76.3 alone.

  • Q77Osteochondrodysplasia with defects of growth of tubular bones and spine
  • E74Other disorders of carbohydrate metabolism

Risk adjustment

E76.3 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 49 Specified Lysosomal Storage Disorders9.256 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

E76.3 is named in 4 Medicare coverage policies 4 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A56500Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A56500Billing and Coding: Cardiac Catheterization and Coronary Angiography

How E76.3 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E76.3.

  • Mucopolysaccharidosis
  • Cardiopathymucopolysaccharidosis
  • Mucopolysaccharidosiscardiopathy

Related codes at this level

Codes that share E76. If E76.3 is not quite right, the correct code is usually one of these.

Questions about E76.3

Is E76.3 a billable ICD-10-CM code?
Yes. E76.3 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E76.3 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.