MCMedicalCodingSoftware
E76.1

E76.1: Mucopolysaccharidosis, type II

Billable / specific codeICD-10-CM

E76.1 is a billable, specific ICD-10-CM code for mucopolysaccharidosis, type ii. It is valid for submission on a claim.

Check E76.1 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Hunter's syndrome

Risk adjustment

E76.1 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 49 Specified Lysosomal Storage Disorders9.256 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

E76.1 is named in 2 Medicare coverage policies: 2 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A56500Billing and Coding: Cardiac Catheterization and Coronary Angiography

Alphabetic index entries that lead here

  • Hunter's›syndrome
  • Mucopolysaccharidosis›Hunter's syndrome
  • Mucopolysaccharidosis›type›II
  • Degeneration, degenerative›brain›in›Hunter's syndrome

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E76

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.