E88.42 — MERRF syndrome
E88.42 is a billable, specific ICD-10-CM code for merrf syndrome. It is valid for submission on a claim.
Code also
Both codes may be needed to describe the encounter fully. Sequencing depends on the reason for the visit.
- progressive myoclonic epilepsy (G40.3-)
Inclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Myoclonic epilepsy associated with ragged-red fibers
Risk adjustment
E88.42 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.
Medicare coverage
E88.42 is named in 1 Medicare coverage policy — 1 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.
- A57224Billing and Coding: Respiratory Care
How E88.42 is indexed
Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E88.42.
- MERRF syndrome(myoclonic epilepsy associated with ragged-red fiber)
- Syndrome›MERRF(myoclonic epilepsy associated with ragged-red fibers)
- Disorder›metabolism NOS›mitochondrial›MERRF syndrome(myoclonic epilepsy associated with ragged-red fibers)
Related codes at this level
Codes that share E88.4. If E88.42 is not quite right, the correct code is usually one of these.
Questions about E88.42
- Is E88.42 a billable ICD-10-CM code?
- Yes. E88.42 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
- Where does E88.42 sit in the tabular list?
- Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).