E88.42
E88.42: MERRF syndrome
Billable / specific codeICD-10-CM
E88.42 is a billable, specific ICD-10-CM code for merrf syndrome. It is valid for submission on a claim.
Check E88.42 with the rest of the claim: free scrubberCode also
Both codes may be needed to describe the encounter fully. Sequencing depends on the reason for the visit.
- progressive myoclonic epilepsy (G40.3-)
Inclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Myoclonic epilepsy associated with ragged-red fibers
Excludes1 inherited from the categories above E88.42
A category’s note binds every code beneath it.
Written on E88.4: Mitochondrial metabolism disorders
Risk adjustment
No CMS-HCC V28 category: this code does not change a RAF score.
Medicare coverage
E88.42 is named in 1 Medicare coverage policy: 1 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.
- A57224Billing and Coding: Respiratory Care
Alphabetic index entries that lead here
- MERRF syndrome(myoclonic epilepsy associated with ragged-red fiber)
- Syndrome›MERRF(myoclonic epilepsy associated with ragged-red fibers)
- Disorder›metabolism NOS›mitochondrial›MERRF syndrome(myoclonic epilepsy associated with ragged-red fibers)
Code history
Unchanged in every release from FY2024 to FY2027.