Is D81.81 a billable ICD-10-CM code?

No. D81.81 is a non-billable header code. Code to a higher level of specificity using one of its child codes.

Where does D81.81 sit in the tabular list?

Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), in the block Certain disorders involving the immune mechanism (D80-D89).

What cannot be coded together with D81.81?

D81.81 carries an Excludes1 note, which means the conditions it lists can never be coded together with it on the same encounter.

D81.81

D81.81 — Biotin-dependent carboxylase deficiency

Non-billable headerICD-10-CM

D81.81 is a non-billable header ICD-10-CM code for biotin-dependent carboxylase deficiency. It cannot be billed on its own: choose one of the more specific child codes below.

Excludes1 — never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

Multiple carboxylase deficiency

Risk adjustment

D81.81 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Code to one of these instead D81.81

3 child codes. Green means billable.

Related codes at this level

Codes that share D81.8. If D81.81 is not quite right, the correct code is usually one of these.

Questions about D81.81

Is D81.81 a billable ICD-10-CM code?: No. D81.81 is a non-billable header code. Code to a higher level of specificity using one of its child codes.
Where does D81.81 sit in the tabular list?: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), in the block Certain disorders involving the immune mechanism (D80-D89).
What cannot be coded together with D81.81?: D81.81 carries an Excludes1 note, which means the conditions it lists can never be coded together with it on the same encounter.