D81.81

D81.81: Biotin-dependent carboxylase deficiency

Non-billable headerICD-10-CM

D81.81 is a non-billable header ICD-10-CM code for biotin-dependent carboxylase deficiency. It cannot be billed on its own: choose one of the more specific child codes below.

Excludes1: never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

Multiple carboxylase deficiency

Excludes1 inherited from the categories above D81.81

A category’s note binds every code beneath it.

Written on D81: Combined immunodeficiencies

autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Other codes that can never be billed with D81.81

Their own Excludes1 notes name this code, so the conflict is not listed above.

E79Disorders of purine and pyrimidine metabolism

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Code history

Unchanged in every release from FY2024 to FY2027.

Code to one of these instead D81.81

3 child codes. Green means billable.