D81.818

D81.818: Other biotin-dependent carboxylase deficiency

Billable / specific codeICD-10-CM

D81.818 is a billable, specific ICD-10-CM code for other biotin-dependent carboxylase deficiency. It is valid for submission on a claim.

Check D81.818 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

Holocarboxylase synthetase deficiency
Other multiple carboxylase deficiency

Excludes1 inherited from the categories above D81.818

A category’s note binds every code beneath it.

Written on D81.81: Biotin-dependent carboxylase deficiency

biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

Written on D81: Combined immunodeficiencies

autosomal recessive agammaglobulinemia (Swiss type) (D80.0)

Other codes that can never be billed with D81.818

Their own Excludes1 notes name this code, so the conflict is not listed above.

E79Disorders of purine and pyrimidine metabolism

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

D81.818 is named in 16 Medicare coverage policies: 16 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

A52996Billing and Coding: Routine Foot Care
A56416Billing and Coding: Assays for Vitamins and Metabolic Function
A56638Billing and Coding: Gastrointestinal Pathogen (GIP) Panels Utilizing Multiplex Nucleic Acid Amplification Techniques (NAATs)
A56642Billing and Coding: Gastrointestinal Pathogen (GIP) Panels Utilizing Multiplex Nucleic Acid Amplification Techniques (NAATs)

Alphabetic index entries that lead here

Immunodeficiency›combined›biotin-dependent carboxylase›holocarboxylase synthetase
Immunodeficiency›combined›biotin-dependent carboxylase›specified type NEC

Code history

Unchanged in every release from FY2024 to FY2027.