E74.02
E74.02: Pompe disease
Billable / specific codeICD-10-CM
E74.02 is a billable, specific ICD-10-CM code for pompe disease. It is valid for submission on a claim.
Check E74.02 with the rest of the claim: free scrubberInclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Cardiac glycogenosis
- Type II glycogen storage disease
Risk adjustment
E74.02 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:
- HCC 49 Specified Lysosomal Storage Disorders9.256 RAF
Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.
Medicare coverage
E74.02 is named in 7 Medicare coverage policies: 7 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.
- A52494High Frequency Chest Wall Oscillation Devices - Policy Article
- A52510Mechanical In-exsufflation Devices - Policy Article
- A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
- A54095Billing and Coding: Nerve Conduction Studies and Electromyography
Alphabetic index entries that lead here
- Cardiomegalia glycogenica diffusa
- Pompe's disease(glycogen storage)
- Cardiomegaly›glycogen
- Cardiomyopathy›glycogen storage
- Deficiency, deficient›lysosomal alpha-1, 4 glucosidase
- Disease, diseased›Pompe's(glycogenosis II)
- Glycogenosis›cardiac
- Myocardiopathy›glycogen storage
- Cardiomyopathy›due to›cardiac glycogenosis
- Disease, diseased›glycogen storage›heart
- Disease, diseased›glycogen storage›lysosomal
- Disease, diseased›glycogen storage›myocardium
Code history
Unchanged in every release from FY2024 to FY2027.