MCMedicalCodingSoftware
E74.01

E74.01: von Gierke disease

Billable / specific codeICD-10-CM

E74.01 is a billable, specific ICD-10-CM code for von gierke disease. It is valid for submission on a claim.

Check E74.01 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Type I glycogen storage disease

Excludes1 inherited from the categories above E74.01

A category’s note binds every code beneath it.

Written on E74: Other disorders of carbohydrate metabolism

Risk adjustment

E74.01 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 50 Amyloidosis, Porphyria, and Other Specified Metabolic Disorders0.648 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

E74.01 is named in 3 Medicare coverage policies: 3 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A56500Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A56619Billing and Coding: Nerve Conduction Studies and Electromyography

Alphabetic index entries that lead here

  • Gierke's disease(glycogenosis I)
  • Van Creveld-von Gierke disease
  • Von Gierke's disease
  • Deficiency, deficient›glucose-6-phosphatase
  • Disease, diseased›Gierke's(glycogenosis I)
  • Disease, diseased›van Creveld-von Gierke(glycogenosis I)
  • Disease, diseased›von Gierke's(glycogenosis I)
  • Disease, diseased›glycogen storage›glucose-6-phosphatase deficiency
  • Disease, diseased›glycogen storage›type I
  • Disease, diseased›glycogen storage›Von Gierke's

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E74.0

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.