E74.01 — von Gierke disease
E74.01 is a billable, specific ICD-10-CM code for von gierke disease. It is valid for submission on a claim.
Inclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Type I glycogen storage disease
Risk adjustment
E74.01 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:
- HCC 50 Amyloidosis, Porphyria, and Other Specified Metabolic Disorders0.648 RAF
Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.
Medicare coverage
E74.01 is named in 5 Medicare coverage policies — 5 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.
- A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
- A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
- A56500Billing and Coding: Cardiac Catheterization and Coronary Angiography
- A56500Billing and Coding: Cardiac Catheterization and Coronary Angiography
How E74.01 is indexed
Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E74.01.
- Gierke's disease(glycogenosis I)
- Van Creveld-von Gierke disease
- Von Gierke's disease
- Deficiency, deficient›glucose-6-phosphatase
- Disease, diseased›Gierke's(glycogenosis I)
- Disease, diseased›van Creveld-von Gierke(glycogenosis I)
- Disease, diseased›von Gierke's(glycogenosis I)
- Disease, diseased›glycogen storage›glucose-6-phosphatase deficiency
- Disease, diseased›glycogen storage›type I
- Disease, diseased›glycogen storage›Von Gierke's
Related codes at this level
Codes that share E74.0. If E74.01 is not quite right, the correct code is usually one of these.
Questions about E74.01
- Is E74.01 a billable ICD-10-CM code?
- Yes. E74.01 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
- Where does E74.01 sit in the tabular list?
- Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).