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D55.1

D55.1Anemia due to other disorders of glutathione metabolism

Billable / specific codeICD-10-CM

D55.1 is a billable, specific ICD-10-CM code for anemia due to other disorders of glutathione metabolism. It is valid for submission on a claim.

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway
  • Anemia (due to) hemolytic nonspherocytic (hereditary), type I

Risk adjustment

D55.1 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

D55.1 is named in 5 Medicare coverage policies 5 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A56718Billing and Coding: Intravenous Immunoglobulin (IVIG)
  • A57110Billing and Coding: MolDX: Blood Product Molecular Antigen Typing
  • A57124Billing and Coding: MolDX: Blood Product Molecular Antigen Typing
  • A57155Billing and Coding: MolDX: Blood Product Molecular Antigen Typing

How D55.1 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to D55.1.

  • Anemiaerythrocytic glutathione deficiency
  • Anemiaglutathione-reductase deficiency
  • Disorderpentose phosphate pathway with anemia
  • Anemiadeficiency6 phosphogluconate dehydrogenase
  • Anemiadeficiency6-PGD
  • Anemiadeficiencyerythrocytic glutathione
  • AnemiadeficiencyG SH
  • AnemiadeficiencyGGS-R
  • Anemiadeficiencyglutathione reductase
  • Anemiadeficiencyenzymerelated to hexose monophosphate shunt pathway NEC(HMP)
  • Anemiadue todisorder ofglutathione metabolism
  • Anemiawithdisorder ofpentose phosphate pathway

Related codes at this level

Codes that share D55. If D55.1 is not quite right, the correct code is usually one of these.

Questions about D55.1

Is D55.1 a billable ICD-10-CM code?
Yes. D55.1 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does D55.1 sit in the tabular list?
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), in the block Hemolytic anemias (D55-D59).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.