E78.3

E78.3: Hyperchylomicronemia

Billable / specific codeICD-10-CM

E78.3 is a billable, specific ICD-10-CM code for hyperchylomicronemia. It is valid for submission on a claim.

Check E78.3 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

Chylomicron retention disease
Fredrickson's hyperlipoproteinemia, type I or V
Hyperlipidemia, group D
Mixed hyperglyceridemia

Excludes1 inherited from the categories above E78.3

A category’s note binds every code beneath it.

Written on E78: Disorders of lipoprotein metabolism and other lipidemias

sphingolipidosis (E75.0-E75.3)

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

E78.3 is named in 9 Medicare coverage policies: 9 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

A56416Billing and Coding: Assays for Vitamins and Metabolic Function
A56422Billing and Coding: Bariatric Surgical Management of Morbid Obesity
A56675Billing and Coding: Homocysteine Level, Serum
A56943Billing and Coding: MolDX: Biomarkers in Cardiovascular Risk Assessment

Alphabetic index entries that lead here

Bürger-Grütz disease or syndrome
Chylomicronemia(fasting) (with hyperprebetalipoproteinemia)
Hyperchylomicronemia(familial) (primary)
Disease, diseased›Bürger-Grütz(essential familial hyperlipemia)
Disease, diseased›chylomicron retention
Frederickson's hyperlipoproteinemia, type›I and V
Hepatosplenomegaly›hyperlipemic(Bürger-Grütz type)
Hyperchylomicronemia›with hyperbetalipoproteinemia
Hyperglyceridemia›mixed
Lipemia›retina, retinalis
Lipidosis›hepatosplenomegalic
Prebetalipoproteinemia›with chylomicronemia

Code history

Unchanged in every release from FY2024 to FY2027.