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E75.244

E75.244Niemann-Pick disease type A/B

Billable / specific codeICD-10-CM

E75.244 is a billable, specific ICD-10-CM code for niemann-pick disease type a/b. It is valid for submission on a claim.

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
  • Chronic neurovisceral acid sphingomyelinase deficiency

Risk adjustment

E75.244 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

E75.244 is named in 17 Medicare coverage policies 17 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A52996Billing and Coding: Routine Foot Care
  • A56232Billing and Coding: Foot Care
  • A56612Billing and Coding: CT of the Head
  • A56680Billing and Coding: Routine Foot Care

How E75.244 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E75.244.

  • Deficiency, deficientchronic neurovisceral acid sphingomyelinase
  • Niemann-Pick disease or syndrometypeA/B
  • Deficiency, deficientacid sphingomyelinasetypeA/B

Related codes at this level

Codes that share E75.24. If E75.244 is not quite right, the correct code is usually one of these.

Questions about E75.244

Is E75.244 a billable ICD-10-CM code?
Yes. E75.244 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E75.244 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.