MCMedicalCodingSoftware
E75.241

E75.241: Niemann-Pick disease type B

Billable / specific codeICD-10-CM

E75.241 is a billable, specific ICD-10-CM code for niemann-pick disease type b. It is valid for submission on a claim.

Check E75.241 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Acid sphingomyelinase deficiency type B (ASMD type B)
  • Chronic visceral acid sphingomyelinase deficiency

Excludes1 inherited from the categories above E75.241

A category’s note binds every code beneath it.

Written on E75.2: Other sphingolipidosis

  • adrenoleukodystrophy [Addison-Schilder] (E71.528)

Written on E75: Disorders of sphingolipid metabolism and other lipid storage disorders

Other codes that can never be billed with E75.241

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • R79Other abnormal findings of blood chemistry

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

E75.241 is named in 10 Medicare coverage policies: 10 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A52996Billing and Coding: Routine Foot Care
  • A56232Billing and Coding: Foot Care
  • A56943Billing and Coding: MolDX: Biomarkers in Cardiovascular Risk Assessment
  • A57037Billing and Coding: MolDX: Biomarkers in Cardiovascular Risk Assessment

Alphabetic index entries that lead here

  • Deficiency, deficient›chronic visceral acid sphingomyelinase
  • Niemann-Pick disease or syndrome›type›B
  • Deficiency, deficient›acid sphingomyelinase›type›B

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E75.24

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.