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E72.19

E72.19: Other disorders of sulfur-bearing amino-acid metabolism

Billable / specific codeICD-10-CM

E72.19 is a billable, specific ICD-10-CM code for other disorders of sulfur-bearing amino-acid metabolism. It is valid for submission on a claim.

Check E72.19 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Cystathioninuria
  • Methioninemia
  • Sulfite oxidase deficiency

Excludes1 inherited from the categories above E72.19

A category’s note binds every code beneath it.

Written on E72.1: Disorders of sulfur-bearing amino-acid metabolism

Written on E72: Other disorders of amino-acid metabolism

  • disorders of:
  • aromatic amino-acid metabolism (E70.-)
  • branched-chain amino-acid metabolism (E71.0-E71.2)
  • fatty-acid metabolism (E71.3)
  • purine and pyrimidine metabolism (E79.-)
  • gout (M1A.-, M10.-)

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

E72.19 is named in 1 Medicare coverage policy: 1 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A56416Billing and Coding: Assays for Vitamins and Metabolic Function

Alphabetic index entries that lead here

  • Cystathioninemia
  • Cystathioninuria
  • Hypermethioninemia
  • Methioninemia
  • Deficiency, deficient›sulfite oxidase
  • Disease, diseased›oast-house-urine
  • Malabsorption›methionine
  • Disorder›amino-acid›cystathioninuria
  • Disturbance›metabolism›cystathionine
  • Disturbance›metabolism›homocystine
  • Disturbance›metabolism›methionine
  • Disorder›metabolism NOS›amino-acid›sulfur-bearing›other specified

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E72.1

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.