E71.0
E71.0: Maple-syrup-urine disease
Billable / specific codeICD-10-CM
E71.0 is a billable, specific ICD-10-CM code for maple-syrup-urine disease. It is valid for submission on a claim.
Check E71.0 with the rest of the claim: free scrubberOther codes that can never be billed with E71.0
Their own Excludes1 notes name this code, so the conflict is not listed above.
- E72Other disorders of amino-acid metabolism
Risk adjustment
No CMS-HCC V28 category: this code does not change a RAF score.
Alphabetic index entries that lead here
- Maple-syrup-urine disease
- Disease, diseased›maple-syrup-urine
- Menkes' disease or syndrome›meaning maple-syrup-urine disease
- Syndrome›maple-syrup-urine
- Disorder›metabolism NOS›amino-acid›branched chain›maple syrup urine disease
Code history
Unchanged in every release from FY2024 to FY2027.