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E71.314

E71.314: Muscle carnitine palmitoyltransferase deficiency

Billable / specific codeICD-10-CM

E71.314 is a billable, specific ICD-10-CM code for muscle carnitine palmitoyltransferase deficiency. It is valid for submission on a claim.

Check E71.314 with the rest of the claim: free scrubber

Excludes1 inherited from the categories above E71.314

A category’s note binds every code beneath it.

Written on E71.3: Disorders of fatty-acid metabolism

  • peroxisomal disorders (E71.5)
  • Refsum's disease (G60.1)
  • Schilder's disease (G37.0)

Excludes2 inherited from the categories above E71.314

Not part of this code, but both may be coded when both are present.

Written on E71.3: Disorders of fatty-acid metabolism

  • carnitine deficiency due to inborn error of metabolism (E71.42)

Other codes that can never be billed with E71.314

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • E71.4Disorders of carnitine metabolism

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

E71.314 is named in 2 Medicare coverage policies: 2 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A54095Billing and Coding: Nerve Conduction Studies and Electromyography
  • A57123Billing and Coding: Nerve Conduction Studies and Electromyography

Alphabetic index entries that lead here

  • Muscle, muscular›carnitine deficiency(palmityltransferase)
  • Deficiency, deficient›carnitine›muscle palmityltransferase
  • Deficiency, deficient›muscle›carnitine(palmityltransferase)

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E71.31

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.