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E71.314

E71.314Muscle carnitine palmitoyltransferase deficiency

Billable / specific codeICD-10-CM

E71.314 is a billable, specific ICD-10-CM code for muscle carnitine palmitoyltransferase deficiency. It is valid for submission on a claim.

Other codes that can never be billed with E71.314

These codes carry an Excludes1 note pointing at E71.314. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E71.314 alone.

  • E71.4Disorders of carnitine metabolism

Risk adjustment

E71.314 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

E71.314 is named in 4 Medicare coverage policies 4 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A54095Billing and Coding: Nerve Conduction Studies and Electromyography
  • A54095Billing and Coding: Nerve Conduction Studies and Electromyography
  • A57123Billing and Coding: Nerve Conduction Studies and Electromyography
  • A57123Billing and Coding: Nerve Conduction Studies and Electromyography

How E71.314 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E71.314.

  • Muscle, muscularcarnitine deficiency(palmityltransferase)
  • Deficiency, deficientcarnitinemuscle palmityltransferase
  • Deficiency, deficientmusclecarnitine(palmityltransferase)

Related codes at this level

Codes that share E71.31. If E71.314 is not quite right, the correct code is usually one of these.

Questions about E71.314

Is E71.314 a billable ICD-10-CM code?
Yes. E71.314 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E71.314 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.