Is E71.42 a billable ICD-10-CM code?

Yes. E71.42 is a billable, specific ICD-10-CM code and is valid for submission on a claim.

Where does E71.42 sit in the tabular list?

Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).

What cannot be coded together with E71.42?

E71.42 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above E71.42 (E71.4) and apply to it just the same.

E71.42

E71.42 — Carnitine deficiency due to inborn errors of metabolism

Billable / specific codeICD-10-CM

E71.42 is a billable, specific ICD-10-CM code for carnitine deficiency due to inborn errors of metabolism. It is valid for submission on a claim.

Code also

Both codes may be needed to describe the encounter fully. Sequencing depends on the reason for the visit.

associated inborn error or metabolism

Excludes1 inherited from the categories above E71.42

These are not written on E71.42, but they bind it: a note on a category applies to every code beneath it. Billing E71.42 with anything listed here is a denial.

Written on E71.4 — Disorders of carnitine metabolism

Muscle carnitine palmitoyltransferase deficiency (E71.314)

Other codes that can never be billed with E71.42

These codes carry an Excludes1 note pointing at E71.42. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E71.42 alone.

E71.511Neonatal adrenoleukodystrophy

Risk adjustment

E71.42 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

E71.42 is named in 5 Medicare coverage policies — 5 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

A54095Billing and Coding: Nerve Conduction Studies and Electromyography
A54095Billing and Coding: Nerve Conduction Studies and Electromyography
A56416Billing and Coding: Assays for Vitamins and Metabolic Function
A57123Billing and Coding: Nerve Conduction Studies and Electromyography

How E71.42 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E71.42.

Deficiency, deficient›carnitine›due to›inborn errors of metabolism

Code history

E71.42 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.

Related codes at this level

Codes that share E71.4. If E71.42 is not quite right, the correct code is usually one of these.

Questions about E71.42

Is E71.42 a billable ICD-10-CM code?: Yes. E71.42 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E71.42 sit in the tabular list?: Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
What cannot be coded together with E71.42?: E71.42 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above E71.42 (E71.4) and apply to it just the same.