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E71.313

E71.313: Glutaric aciduria type II

Billable / specific codeICD-10-CM

E71.313 is a billable, specific ICD-10-CM code for glutaric aciduria type ii. It is valid for submission on a claim.

Check E71.313 with the rest of the claim: free scrubber

Excludes1: never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • glutaric aciduria (type 1) NOS (E72.3)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Glutaric aciduria type II A
  • Glutaric aciduria type II B
  • Glutaric aciduria type II C

Excludes1 inherited from the categories above E71.313

A category’s note binds every code beneath it.

Written on E71.3: Disorders of fatty-acid metabolism

  • peroxisomal disorders (E71.5)
  • Refsum's disease (G60.1)
  • Schilder's disease (G37.0)

Excludes2 inherited from the categories above E71.313

Not part of this code, but both may be coded when both are present.

Written on E71.3: Disorders of fatty-acid metabolism

  • carnitine deficiency due to inborn error of metabolism (E71.42)

Other codes that can never be billed with E71.313

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • E72.3Disorders of lysine and hydroxylysine metabolism

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Alphabetic index entries that lead here

  • Aciduria›glutaric›type II

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E71.31

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.