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E71.313

E71.313Glutaric aciduria type II

Billable / specific codeICD-10-CM

E71.313 is a billable, specific ICD-10-CM code for glutaric aciduria type ii. It is valid for submission on a claim.

Excludes1 — never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • glutaric aciduria (type 1) NOS (E72.3)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Glutaric aciduria type II A
  • Glutaric aciduria type II B
  • Glutaric aciduria type II C

Excludes1 inherited from the categories above E71.313

These are not written on E71.313, but they bind it: a note on a category applies to every code beneath it. Billing E71.313 with anything listed here is a denial.

Written on E71.3 Disorders of fatty-acid metabolism

  • peroxisomal disorders (E71.5)
  • Refsum's disease (G60.1)
  • Schilder's disease (G37.0)

Excludes2 inherited from the categories above E71.313

Also inherited, and the opposite of Excludes1: these conditions are not part of E71.313, but a patient can have both, so you may code both.

Written on E71.3 Disorders of fatty-acid metabolism

  • carnitine deficiency due to inborn error of metabolism (E71.42)

Other codes that can never be billed with E71.313

These codes carry an Excludes1 note pointing at E71.313. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E71.313 alone.

  • E72.3Disorders of lysine and hydroxylysine metabolism

Risk adjustment

E71.313 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

How E71.313 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E71.313.

  • Aciduriaglutarictype II

Code history

E71.313 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.

Related codes at this level

Codes that share E71.31. If E71.313 is not quite right, the correct code is usually one of these.

Questions about E71.313

Is E71.313 a billable ICD-10-CM code?
Yes. E71.313 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E71.313 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
What cannot be coded together with E71.313?
E71.313 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above E71.313 (E71.3) and apply to it just the same.
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.