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D82.1

D82.1Di George's syndrome

Billable / specific codeICD-10-CM

D82.1 is a billable, specific ICD-10-CM code for di george's syndrome. It is valid for submission on a claim.

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Pharyngeal pouch syndrome
  • Thymic alymphoplasia
  • Thymic aplasia or hypoplasia with immunodeficiency

Other codes that can never be billed with D82.1

These codes carry an Excludes1 note pointing at D82.1. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading D82.1 alone.

  • Q38.7Congenital pharyngeal pouch
  • E32.8Other diseases of thymus
  • E20Hypoparathyroidism
  • E32Diseases of thymus

Risk adjustment

D82.1 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 115 Specified Immunodeficiencies and White Blood Cell Disorders0.565 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

D82.1 is named in 35 Medicare coverage policies 35 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A52507External Infusion Pumps - Policy Article
  • A52509Intravenous Immune Globulin - Policy Article
  • A54660Billing and Coding: Coverage of Intravenous Immune Globulin for Treatment of Primary Immune Deficiency Diseases in the Home – Medicare Benefit Policy Manual, Chapter 15, 50.6
  • A55717Billing and Coding: Lab: Flow Cytometry

How D82.1 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to D82.1.

  • Alymphoplasia, thymic
  • Di George's syndrome
  • DiGeorge's syndrome(thymic hypoplasia)
  • Pharyngeal pouch syndrome
  • Alymphocytosisthymic(with immunodeficiency)
  • Aplasiaparathyroid-thymic
  • Aplasiathymic, with immunodeficiency
  • Dysplasiathymic, with immunodeficiency
  • Hypoplasia, hypoplasticthymic, with immunodeficiency
  • Syndromedi George's
  • Syndromepharyngeal pouch
  • Hypoplasia, hypoplasticthymuswith immunodeficiency

Related codes at this level

Codes that share D82. If D82.1 is not quite right, the correct code is usually one of these.

Questions about D82.1

Is D82.1 a billable ICD-10-CM code?
Yes. D82.1 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does D82.1 sit in the tabular list?
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), in the block Certain disorders involving the immune mechanism (D80-D89).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.