G11.3

G11.3: Cerebellar ataxia with defective DNA repair

Billable / specific codeICD-10-CM

G11.3 is a billable, specific ICD-10-CM code for cerebellar ataxia with defective dna repair. It is valid for submission on a claim.

Check G11.3 with the rest of the claim: free scrubber

Excludes2: not included here, but may coexist

The excluded condition is not part of this code, but a patient can have both. You may code both.

Cockayne's syndrome (Q87.19)
other disorders of purine and pyrimidine metabolism (E79.-)
xeroderma pigmentosum (Q82.1)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

Ataxia telangiectasia [Louis-Bar]

Excludes2 inherited from the categories above G11.3

Not part of this code, but both may be coded when both are present.

Written on G11: Hereditary ataxia

cerebral palsy (G80.-)
hereditary and idiopathic neuropathy (G60.-)
metabolic disorders (E70-E88)

Other codes that can never be billed with G11.3

Their own Excludes1 notes name this code, so the conflict is not listed above.

D82Immunodeficiency associated with other major defects
E31Polyglandular dysfunction
Q85Phakomatoses, not elsewhere classified
R26Abnormalities of gait and mobility
R27Other lack of coordination

Risk adjustment

G11.3 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

HCC 200 Friedreich and Other Hereditary Ataxias; Huntington Disease0.279 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

G11.3 is named in 24 Medicare coverage policies: 24 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

A52507External Infusion Pumps - Policy Article
A52509Intravenous Immune Globulin - Policy Article
A53057Billing and Coding: Home Health Occupational Therapy
A53064Billing and Coding: Outpatient Occupational Therapy

Alphabetic index entries that lead here

Ataxia-telangiectasia(Louis-Bar)
Boder-Sedgwick syndrome(ataxia-telangiectasia)
Louis-Bar syndrome(ataxia-telangiectasia)
Ataxia, ataxy, ataxic›telangiectasia(Louis-Bar)
Syndrome›ataxia-telangiectasia
Syndrome›Boder-Sedgewick
Syndrome›Louis-Barré
Telangiectasia, telangiectasis›ataxic(cerebellar) (Louis-Bar)
Ataxia, ataxy, ataxic›cerebellar›with defective DNA repair

Code history

Unchanged in every release from FY2024 to FY2027.