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Q87.19

Q87.19: Other congenital malformation syndromes predominantly associated with short stature

Billable / specific codeICD-10-CMPOA exempt

Q87.19 is a billable, specific ICD-10-CM code for other congenital malformation syndromes predominantly associated with short stature. It is valid for submission on a claim.

Check Q87.19 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Aarskog syndrome
  • Cockayne syndrome
  • De Lange syndrome
  • Dubowitz syndrome
  • Noonan syndrome
  • Robinow-Silverman-Smith syndrome
  • Russell-Silver syndrome
  • Seckel syndrome

Excludes1 inherited from the categories above Q87.19

A category’s note binds every code beneath it.

Written on Q87.1: Congenital malformation syndromes predominantly associated with short stature

  • Ellis-van Creveld syndrome (Q77.6)
  • Smith-Lemli-Opitz syndrome (E78.72)

Other codes that can never be billed with Q87.19

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • E23.3Hypothalamic dysfunction, not elsewhere classified
  • E34.3Short stature due to endocrine disorder
  • Q67Congenital musculoskeletal deformities of head, face, spine and chest
  • Q75Other congenital malformations of skull and face bones
  • Q81.0Epidermolysis bullosa simplex
  • Q89.7Multiple congenital malformations, not elsewhere classified
  • Q96Turner's syndrome
  • E79Disorders of purine and pyrimidine metabolism

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

Q87.19 is named in 2 Medicare coverage policies: 2 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A53060Billing and Coding: Ophthalmology: Extended Ophthalmoscopy and Fundus Photography
  • A56726Billing and Coding: Ophthalmology: Posterior Segment Imaging (Extended Ophthalmoscopy and Fundus Photography)

Alphabetic index entries that lead here

  • Aarskog's syndrome
  • Amsterdam dwarfism
  • Bonnevie-Ullrich syndrome
  • Bruck-de Lange disease
  • Cockayne's syndrome
  • Cornelia de Lange syndrome
  • De Lange's syndrome
  • Dubowitz' syndrome
  • Noonan's syndrome
  • Prader-Willi-like syndrome
  • Robinow-Silverman-Smith syndrome
  • Russell-Silver syndrome

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under Q87.1

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.