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Q82.2

Q82.2Congenital cutaneous mastocytosis

Billable / specific codeICD-10-CMPOA exempt

Q82.2 is a billable, specific ICD-10-CM code for congenital cutaneous mastocytosis. It is valid for submission on a claim.

Excludes1 — never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • cutaneous mastocytosis NOS (D47.01)
  • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
  • malignant mastocytosis (C96.2-)
  • systemic mastocytosis (D47.02)
  • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Congenital diffuse cutaneous mastocytosis
  • Congenital maculopapular cutaneous mastocytosis
  • Congenital urticaria pigmentosa

Excludes1 inherited from the categories above Q82.2

These are not written on Q82.2, but they bind it: a note on a category applies to every code beneath it. Billing Q82.2 with anything listed here is a denial.

Written on Q82 Other congenital malformations of skin

  • acrodermatitis enteropathica (E83.2)
  • congenital erythropoietic porphyria (E80.0)
  • pilonidal cyst or sinus (L05.-)
  • Sturge-Weber (-Dimitri) syndrome (Q85.89)

Other codes that can never be billed with Q82.2

These codes carry an Excludes1 note pointing at Q82.2. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading Q82.2 alone.

  • C96.2Malignant mast cell neoplasm
  • D47.0Mast cell neoplasms of uncertain behavior
  • D47.01Cutaneous mastocytosis
  • D89.4Mast cell activation syndrome and related disorders

Risk adjustment

Q82.2 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

Q82.2 is named in 13 Medicare coverage policies 13 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A57044Billing and Coding: Removal of Benign Skin Lesions
  • A57837Billing and Coding: MolDX: Next-Generation Sequencing Lab-Developed Tests for Myeloid Malignancies and Suspected Myeloid Malignancies
  • A57873Billing and Coding: MolDX: Next-Generation Sequencing Lab-Developed Tests for Myeloid Malignancies and Suspected Myeloid Malignancies
  • A57878Billing and Coding: MolDX: Next-Generation Sequencing Lab-Developed Tests for Myeloid Malignancies and Suspected Myeloid Malignancies

How Q82.2 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to Q82.2.

  • Mastocytosiscutaneouscongenital
  • Mastocytosiscutaneousof neonatal onset
  • Mastocytosiscutaneousof newborn onset
  • Urticariapigmentosacongenital
  • Urticariapigmentosaof neonatal onset
  • Urticariapigmentosaof newborn onset

Code history

Q82.2 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.

Related codes at this level

Codes that share Q82. If Q82.2 is not quite right, the correct code is usually one of these.

Questions about Q82.2

Is Q82.2 a billable ICD-10-CM code?
Yes. Q82.2 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does Q82.2 sit in the tabular list?
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0), in the block Other congenital malformations (Q80-Q89).
What cannot be coded together with Q82.2?
Q82.2 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above Q82.2 (Q82) and apply to it just the same.
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.