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D47.01

D47.01: Cutaneous mastocytosis

Billable / specific codeICD-10-CM

D47.01 is a billable, specific ICD-10-CM code for cutaneous mastocytosis. It is valid for submission on a claim.

Check D47.01 with the rest of the claim: free scrubber

Excludes1: never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa

Excludes1 inherited from the categories above D47.01

A category’s note binds every code beneath it.

Written on D47.0: Mast cell neoplasms of uncertain behavior

  • congenital cutaneous mastocytosis (Q82.2)
  • histiocytic neoplasms of uncertain behavior (D47.Z9)
  • malignant mast cell neoplasm (C96.2-)

Other codes that can never be billed with D47.01

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • D89.4Mast cell activation syndrome and related disorders
  • L50Urticaria
  • Q82.2Congenital cutaneous mastocytosis

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

D47.01 is named in 22 Medicare coverage policies: 22 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A52480Oral Antiemetic Drugs (Replacement for Intravenous Antiemetics) - Policy Article
  • A55717Billing and Coding: Lab: Flow Cytometry
  • A56199Billing and Coding: Molecular Pathology Procedures
  • A56346Billing and Coding: Removal of Benign and Malignant Skin Lesions

Alphabetic index entries that lead here

  • Mastocytoma›solitary
  • Mastocytosis›cutaneous(diffuse) (maculopapular)
  • Telangiectasia, telangiectasis›macularis eruptiva perstans
  • Urticaria›pigmentosa

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under D47.0

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.