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D47.01

D47.01Cutaneous mastocytosis

Billable / specific codeICD-10-CM

D47.01 is a billable, specific ICD-10-CM code for cutaneous mastocytosis. It is valid for submission on a claim.

Excludes1 — never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa

Excludes1 inherited from the categories above D47.01

These are not written on D47.01, but they bind it: a note on a category applies to every code beneath it. Billing D47.01 with anything listed here is a denial.

Written on D47.0 Mast cell neoplasms of uncertain behavior

  • congenital cutaneous mastocytosis (Q82.2)
  • histiocytic neoplasms of uncertain behavior (D47.Z9)
  • malignant mast cell neoplasm (C96.2-)

Other codes that can never be billed with D47.01

These codes carry an Excludes1 note pointing at D47.01. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading D47.01 alone.

  • L50Urticaria
  • D89.4Mast cell activation syndrome and related disorders
  • Q82.2Congenital cutaneous mastocytosis

Risk adjustment

D47.01 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

D47.01 is named in 26 Medicare coverage policies 26 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

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How D47.01 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to D47.01.

  • Mastocytomasolitary
  • Mastocytosiscutaneous(diffuse) (maculopapular)
  • Telangiectasia, telangiectasismacularis eruptiva perstans
  • Urticariapigmentosa

Code history

D47.01 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.

Related codes at this level

Codes that share D47.0. If D47.01 is not quite right, the correct code is usually one of these.

Questions about D47.01

Is D47.01 a billable ICD-10-CM code?
Yes. D47.01 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does D47.01 sit in the tabular list?
Neoplasms (C00-D49), in the block Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes (D37-D48).
What cannot be coded together with D47.01?
D47.01 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above D47.01 (D47.0) and apply to it just the same.
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.