E80.0 — Hereditary erythropoietic porphyria
E80.0 is a billable, specific ICD-10-CM code for hereditary erythropoietic porphyria. It is valid for submission on a claim.
Inclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Congenital erythropoietic porphyria
- Erythropoietic protoporphyria
Other codes that can never be billed with E80.0
These codes carry an Excludes1 note pointing at E80.0. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E80.0 alone.
- Q82Other congenital malformations of skin
Risk adjustment
E80.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:
- HCC 50 Amyloidosis, Porphyria, and Other Specified Metabolic Disorders0.648 RAF
Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.
Medicare coverage
E80.0 is named in 6 Medicare coverage policies — 6 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.
- A57181Billing and Coding: Allergy Testing
- A60360Billing and Coding: Allergy Diagnostic Testing
- A60363Billing and Coding: Allergy Diagnostic Testing
- A60374Billing and Coding: Allergy Diagnostic Testing
How E80.0 is indexed
Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E80.0.
- Protoporphyria, erythropoietic
- Porphyria›erythropoietic(congenital) (hereditary)
Related codes at this level
Codes that share E80. If E80.0 is not quite right, the correct code is usually one of these.
Questions about E80.0
- Is E80.0 a billable ICD-10-CM code?
- Yes. E80.0 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
- Where does E80.0 sit in the tabular list?
- Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).