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E80.0

E80.0: Hereditary erythropoietic porphyria

Billable / specific codeICD-10-CM

E80.0 is a billable, specific ICD-10-CM code for hereditary erythropoietic porphyria. It is valid for submission on a claim.

Check E80.0 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Congenital erythropoietic porphyria
  • Erythropoietic protoporphyria

Other codes that can never be billed with E80.0

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • Q82Other congenital malformations of skin

Risk adjustment

E80.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 50 Amyloidosis, Porphyria, and Other Specified Metabolic Disorders0.648 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

E80.0 is named in 10 Medicare coverage policies: 10 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A60360Billing and Coding: Allergy Diagnostic Testing
  • A60361Billing and Coding: Allergy Diagnostic Testing
  • A60363Billing and Coding: Allergy Diagnostic Testing
  • A60364Billing and Coding: Allergy Diagnostic Testing

Alphabetic index entries that lead here

  • Protoporphyria, erythropoietic
  • Porphyria›erythropoietic(congenital) (hereditary)

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E80

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.