MCMedicalCodingSoftware
E83.01

E83.01: Wilson's disease

Billable / specific codeICD-10-CM

E83.01 is a billable, specific ICD-10-CM code for wilson's disease. It is valid for submission on a claim.

Check E83.01 with the rest of the claim: free scrubber

Code also

Both codes may be needed to describe the encounter fully. Sequencing depends on the reason for the visit.

  • associated Kayser Fleischer ring (H18.04-)

Excludes1 inherited from the categories above E83.01

A category’s note binds every code beneath it.

Written on E83: Disorders of mineral metabolism

  • dietary mineral deficiency (E58-E61)
  • parathyroid disorders (E20-E21)
  • vitamin D deficiency (E55.-)

Other codes that can never be billed with E83.01

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • E61Deficiency of other nutrient elements
  • R79.0Abnormal level of blood mineral

Risk adjustment

E83.01 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 50 Amyloidosis, Porphyria, and Other Specified Metabolic Disorders0.648 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

E83.01 is named in 3 Medicare coverage policies: 3 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A56199Billing and Coding: Molecular Pathology Procedures
  • A56868Billing and Coding: Outpatient Speech Language Pathology
  • A60409Billing and Coding: Molecular Pathology Procedures

Alphabetic index entries that lead here

  • Hepatolenticular degeneration
  • Kinnier Wilson's disease(hepatolenticular degeneration)
  • Lenticular degeneration, progressive
  • Strümpell-Westphal pseudosclerosis
  • Westphal-Strümpell syndrome
  • Deficiency, deficient›ceruloplasmin(Wilson)
  • Degeneration, degenerative›hepatolenticular(Wilson's)
  • Degeneration, degenerative›lenticular(familial) (progressive) (Wilson's) (with cirrhosis of liver)
  • Degeneration, degenerative›Wilson's hepatolenticular
  • Disease, diseased›hepatolenticular
  • Disease, diseased›Kinnier Wilson's(hepatolenticular degeneration)
  • Disease, diseased›Wilson's(hepatolenticular degeneration)

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E83.0

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.