E75.4 — Neuronal ceroid lipofuscinosis
E75.4 is a billable, specific ICD-10-CM code for neuronal ceroid lipofuscinosis. It is valid for submission on a claim.
Inclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Batten disease
- Bielschowsky-Jansky disease
- Kufs disease
- Spielmeyer-Vogt disease
Risk adjustment
E75.4 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.
Medicare coverage
E75.4 is named in 3 Medicare coverage policies — 3 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.
- A56612Billing and Coding: CT of the Head
- A56868Billing and Coding: Outpatient Speech Language Pathology
- A57204Billing and Coding: MRI and CT Scans of the Head and Neck
How E75.4 is indexed
Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E75.4.
- Amaurotic idiocy(infantile) (juvenile) (late)
- Batten disease(-Mayou)
- Bielschowsky disease(-Jansky)
- Ceroid-lipofuscinosis, neuronal
- Jansky-Bielschowsky amaurotic idiocy
- Kufs' disease
- Lipofuscinosis, neuronal(with ceroidosis)
- Spielmeyer-Vogt disease
- Vogt-Spielmeyer amaurotic idiocy or disease
- Batten disease›retina
- Idiot, idiocy›amaurotic(Bielschowsky(-Jansky)) (family) (infantile (late)) (juvenile (late)) (Vogt-Spielmeyer)
- Lipidosis›cerebral(infantile) (juvenile) (late)
Related codes at this level
Codes that share E75. If E75.4 is not quite right, the correct code is usually one of these.
Questions about E75.4
- Is E75.4 a billable ICD-10-CM code?
- Yes. E75.4 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
- Where does E75.4 sit in the tabular list?
- Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).