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E75.01

E75.01Sandhoff disease

Billable / specific codeICD-10-CM

E75.01 is a billable, specific ICD-10-CM code for sandhoff disease. It is valid for submission on a claim.

Risk adjustment

E75.01 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

E75.01 is named in 3 Medicare coverage policies 3 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A56612Billing and Coding: CT of the Head
  • A56868Billing and Coding: Outpatient Speech Language Pathology
  • A57204Billing and Coding: MRI and CT Scans of the Head and Neck

How E75.01 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E75.01.

  • Sandhoff's disease
  • GangliosidosisGM2Sandhoff disease

Related codes at this level

Codes that share E75.0. If E75.01 is not quite right, the correct code is usually one of these.

Questions about E75.01

Is E75.01 a billable ICD-10-CM code?
Yes. E75.01 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E75.01 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.