D74.0 — Congenital methemoglobinemia
D74.0 is a billable, specific ICD-10-CM code for congenital methemoglobinemia. It is valid for submission on a claim.
Inclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Congenital NADH-methemoglobin reductase deficiency
- Hemoglobin-M [Hb-M] disease
- Methemoglobinemia, hereditary
Other codes that can never be billed with D74.0
These codes carry an Excludes1 note pointing at D74.0. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading D74.0 alone.
- D58.2Other hemoglobinopathies
Risk adjustment
D74.0 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.
How D74.0 is indexed
Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to D74.0.
- Deficiency, deficient›NADH diaphorase or reductase(congenital)
- Deficiency, deficient›NADH-methemoglobin reductase(congenital)
- Disease, diseased›diaphorase deficiency
- Methemoglobinemia›congenital
- Methemoglobinemia›enzymatic(congenital)
- Methemoglobinemia›Hb M disease
- Methemoglobinemia›hereditary
- Disease, diseased›hemoglobin or Hb›M
Related codes at this level
Codes that share D74. If D74.0 is not quite right, the correct code is usually one of these.
Questions about D74.0
- Is D74.0 a billable ICD-10-CM code?
- Yes. D74.0 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
- Where does D74.0 sit in the tabular list?
- Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), in the block Other disorders of blood and blood-forming organs (D70-D77).