D68.1 — Hereditary factor XI deficiency
D68.1 is a billable, specific ICD-10-CM code for hereditary factor xi deficiency. It is valid for submission on a claim.
Inclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Hemophilia C
- Plasma thromboplastin antecedent [PTA] deficiency
- Rosenthal's disease
Excludes1 inherited from the categories above D68.1
These are not written on D68.1, but they bind it: a note on a category applies to every code beneath it. Billing D68.1 with anything listed here is a denial.
Excludes2 inherited from the categories above D68.1
Also inherited, and the opposite of Excludes1: these conditions are not part of D68.1, but a patient can have both, so you may code both.
Other codes that can never be billed with D68.1
These codes carry an Excludes1 note pointing at D68.1. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading D68.1 alone.
- R79.1Abnormal coagulation profile
Risk adjustment
D68.1 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:
- HCC 112 Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions0.450 RAF
Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.
Medicare coverage
D68.1 is named in 1 Medicare coverage policy — 1 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.
- A57954Billing and Coding: Routine Foot Care
How D68.1 is indexed
Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to D68.1.
- Rosenthal's disease or syndrome
- Deficiency, deficient›PTA(plasma thromboplastin antecedent)
- Disease, diseased›Rosenthal's(factor XI deficiency)
- Hemophilia›C
- Deficiency, deficient›factor›XI(congenital) (hereditary)
- Deficiency, deficient›plasma thromboplastin›antecedent(PTA)
- Deficiency, deficient›anti-hemophilic›factor›C
Code history
D68.1 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.
Related codes at this level
Codes that share D68. If D68.1 is not quite right, the correct code is usually one of these.
- D68.0Von Willebrand disease
- D68.2Hereditary deficiency of other clotting factors
- D68.3Hemorrhagic disorder due to circulating anticoagulants
- D68.4Acquired coagulation factor deficiency
- D68.5Primary thrombophilia
- D68.6Other thrombophilia
- D68.8Other specified coagulation defects
- D68.9Coagulation defect, unspecified
Questions about D68.1
- Is D68.1 a billable ICD-10-CM code?
- Yes. D68.1 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
- Where does D68.1 sit in the tabular list?
- Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), in the block Coagulation defects, purpura and other hemorrhagic conditions (D65-D69).
- What cannot be coded together with D68.1?
- D68.1 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above D68.1 (D68) and apply to it just the same.