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Q87.A

Q87.A: Loeys-Dietz syndrome

Billable / specific codeICD-10-CMPOA exempt

Q87.A is a billable, specific ICD-10-CM code for loeys-dietz syndrome. It is valid for submission on a claim.

Check Q87.A with the rest of the claim: free scrubber

Excludes1: never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • arterial tortuosity syndrome (Q87.82)
  • Ehlers-Danlos syndrome (Q79.6)
  • Marfan syndrome (Q87.40-Q87.43)
  • other systemic involvement of connective tissue (M35)

Other codes that can never be billed with Q87.A

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • Q67Congenital musculoskeletal deformities of head, face, spine and chest
  • Q75Other congenital malformations of skull and face bones
  • Q89.7Multiple congenital malformations, not elsewhere classified

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

Q87.A is named in 4 Medicare coverage policies: 4 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A59847Billing and Coding: MolDX: Genetic Testing in Heritable Thoracic Aortic Disease
  • A59860Billing and Coding: MolDX: Genetic Testing in Heritable Thoracic Aortic Disease
  • A59868Billing and Coding: MolDX: Genetic Testing in Heritable Thoracic Aortic Disease
  • A59908Billing and Coding: MolDX: Genetic Testing in Heritable Thoracic Aortic Disease

Alphabetic index entries that lead here

  • Syndrome›Loeys-Dietz

Code history

  • addedFY2024-FY2027

    Loeys-Dietz syndrome

Other codes under Q87

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.