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Q87.2

Q87.2Congenital malformation syndromes predominantly involving limbs

Billable / specific codeICD-10-CMPOA exempt

Q87.2 is a billable, specific ICD-10-CM code for congenital malformation syndromes predominantly involving limbs. It is valid for submission on a claim.

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Holt-Oram syndrome
  • Klippel-Trenaunay-Weber syndrome
  • Nail patella syndrome
  • Rubinstein-Taybi syndrome
  • Sirenomelia syndrome
  • Thrombocytopenia with absent radius [TAR] syndrome
  • VATER syndrome

Other codes that can never be billed with Q87.2

These codes carry an Excludes1 note pointing at Q87.2. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading Q87.2 alone.

  • Q74.1Congenital malformation of knee
  • Q84.3Anonychia

Risk adjustment

Q87.2 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

Q87.2 is named in 3 Medicare coverage policies 3 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A53060Billing and Coding: Ophthalmology: Extended Ophthalmoscopy and Fundus Photography
  • A56726Billing and Coding: Ophthalmology: Posterior Segment Imaging (Extended Ophthalmoscopy and Fundus Photography)
  • A57071Billing and Coding: Ophthalmology: Posterior Segment Imaging (Extended Ophthalmoscopy and Fundus Photography)

How Q87.2 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to Q87.2.

  • Fong's syndrome(hereditary osteo-onychodysplasia)
  • Holt-Oram syndrome
  • Klippel-Trenaunay syndrome(-Weber)
  • Mietens' syndrome
  • Onycho-osteodysplasia
  • Osteo-onycho-arthro-dysplasia
  • Osteo-onychodysplasia, hereditary
  • Österreicher-Turner syndrome
  • Rubinstein-Taybi syndrome
  • Sirenomelia(syndrome)
  • TAR syndrome(thrombocytopenia with absent radius)
  • Taybi's syndrome

Related codes at this level

Codes that share Q87. If Q87.2 is not quite right, the correct code is usually one of these.

Questions about Q87.2

Is Q87.2 a billable ICD-10-CM code?
Yes. Q87.2 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does Q87.2 sit in the tabular list?
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0), in the block Other congenital malformations (Q80-Q89).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.