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J43.0

J43.0Unilateral pulmonary emphysema [MacLeod's syndrome]

Billable / specific codeICD-10-CM

J43.0 is a billable, specific ICD-10-CM code for unilateral pulmonary emphysema [macleod's syndrome]. It is valid for submission on a claim.

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Swyer-James syndrome
  • Unilateral emphysema
  • Unilateral hyperlucent lung
  • Unilateral pulmonary artery functional hypoplasia
  • Unilateral transparency of lung

Risk adjustment

J43.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 280 Chronic Obstructive Pulmonary Disease, Interstitial Lung Disorders, and Other Chronic Lung Disorders0.319 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

J43.0 is named in 30 Medicare coverage policies 28 listing it as supporting medical necessity, and 2 listing it as NOT covered. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A56566Billing and Coding: Outpatient Physical and Occupational Therapy Servicesnot covered
  • A57067Billing and Coding: Outpatient Physical and Occupational Therapy Servicesnot covered
  • A52466Nebulizers - Policy Article
  • A52466Nebulizers - Policy Article

How J43.0 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to J43.0.

  • Hyperlucent lung, unilateral
  • MacLeod's syndrome
  • Transparency, lung, unilateral
  • Emphysemaunilateral
  • Hypoplasia, hypoplasticpulmonaryartery, functional
  • Hypoplasia, hypoplasticarterypulmonaryfunctional, unilateral

Related codes at this level

Codes that share J43. If J43.0 is not quite right, the correct code is usually one of these.

Questions about J43.0

Is J43.0 a billable ICD-10-CM code?
Yes. J43.0 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does J43.0 sit in the tabular list?
Diseases of the respiratory system (J00-J99), in the block Chronic lower respiratory diseases (J40-J4A).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.