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E84.0

E84.0Cystic fibrosis with pulmonary manifestations

Billable / specific codeICD-10-CM

E84.0 is a billable, specific ICD-10-CM code for cystic fibrosis with pulmonary manifestations. It is valid for submission on a claim.

Use additional code

Add a secondary code to capture the detail described below.

  • code to identify any infectious organism present, such as:
  • Pseudomonas (B96.5)

Other codes that can never be billed with E84.0

These codes carry an Excludes1 note pointing at E84.0. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E84.0 alone.

  • P78Other perinatal digestive system disorders
  • Q33.0Congenital cystic lung
  • Q45.3Other congenital malformations of pancreas and pancreatic duct
  • J99Respiratory disorders in diseases classified elsewhere

Risk adjustment

E84.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 277 Cystic Fibrosis0.998 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

E84.0 is named in 38 Medicare coverage policies 36 listing it as supporting medical necessity, and 2 listing it as NOT covered. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A56566Billing and Coding: Outpatient Physical and Occupational Therapy Servicesnot covered
  • A57067Billing and Coding: Outpatient Physical and Occupational Therapy Servicesnot covered
  • A52466Nebulizers - Policy Article
  • A52466Nebulizers - Policy Article

How E84.0 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E84.0.

  • Fibrosis, fibroticcysticwithpulmonary manifestations

Related codes at this level

Codes that share E84. If E84.0 is not quite right, the correct code is usually one of these.

Questions about E84.0

Is E84.0 a billable ICD-10-CM code?
Yes. E84.0 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E84.0 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.