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E78.010

E78.010: Homozygous familial hypercholesterolemia [HoFH]

Billable / specific codeICD-10-CM

E78.010 is a billable, specific ICD-10-CM code for homozygous familial hypercholesterolemia [hofh]. It is valid for submission on a claim.

Check E78.010 with the rest of the claim: free scrubber

Excludes1 inherited from the categories above E78.010

A category’s note binds every code beneath it.

Written on E78: Disorders of lipoprotein metabolism and other lipidemias

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

E78.010 is named in 19 Medicare coverage policies: 19 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A54543Therapeutic Apheresis for Familial Hypercholesterolemia
  • A56289Billing and Coding: Therapeutic Apheresis for Familial Hypercholesterolemia
  • A56416Billing and Coding: Assays for Vitamins and Metabolic Function
  • A56422Billing and Coding: Bariatric Surgical Management of Morbid Obesity

Alphabetic index entries that lead here

  • HoFH(homozygous familial hypercholesterolemia)
  • Cholesterolemia›familial›homozygous
  • Hypercholesterolemia›familial›homozygous [HoFH]

Code history

  • addedFY2024-FY2027

    Homozygous familial hypercholesterolemia [HoFH]

Other codes under E78.01

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.