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E71.540

E71.540Rhizomelic chondrodysplasia punctata

Billable / specific codeICD-10-CM

E71.540 is a billable, specific ICD-10-CM code for rhizomelic chondrodysplasia punctata. It is valid for submission on a claim.

Other codes that can never be billed with E71.540

These codes carry an Excludes1 note pointing at E71.540. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E71.540 alone.

  • Q77.3Chondrodysplasia punctata

Risk adjustment

E71.540 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

E71.540 is named in 1 Medicare coverage policy 1 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A56773Billing and Coding: Neurophysiology Evoked Potentials (NEPs)

How E71.540 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E71.540.

  • Rhizomelic chondrodysplasia punctata
  • Disorderperoxisomalrhizomelic chondrodysplasia punctata

Related codes at this level

Codes that share E71.54. If E71.540 is not quite right, the correct code is usually one of these.

Questions about E71.540

Is E71.540 a billable ICD-10-CM code?
Yes. E71.540 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E71.540 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.