Is E71.540 a billable ICD-10-CM code?

Yes. E71.540 is a billable, specific ICD-10-CM code and is valid for submission on a claim.

Where does E71.540 sit in the tabular list?

Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).

What cannot be coded together with E71.540?

E71.540 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above E71.540 (E71.5) and apply to it just the same.

E71.540

E71.540 — Rhizomelic chondrodysplasia punctata

Billable / specific codeICD-10-CM

E71.540 is a billable, specific ICD-10-CM code for rhizomelic chondrodysplasia punctata. It is valid for submission on a claim.

Excludes1 inherited from the categories above E71.540

These are not written on E71.540, but they bind it: a note on a category applies to every code beneath it. Billing E71.540 with anything listed here is a denial.

Written on E71.5 — Peroxisomal disorders

Schilder's disease (G37.0)

Other codes that can never be billed with E71.540

These codes carry an Excludes1 note pointing at E71.540. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading E71.540 alone.

Q77.3Chondrodysplasia punctata

Risk adjustment

E71.540 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

E71.540 is named in 1 Medicare coverage policy — 1 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

A56773Billing and Coding: Neurophysiology Evoked Potentials (NEPs)

How E71.540 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E71.540.

Rhizomelic chondrodysplasia punctata
Disorder›peroxisomal›rhizomelic chondrodysplasia punctata

Code history

E71.540 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.

Related codes at this level

Codes that share E71.54. If E71.540 is not quite right, the correct code is usually one of these.

Questions about E71.540

Is E71.540 a billable ICD-10-CM code?: Yes. E71.540 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E71.540 sit in the tabular list?: Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
What cannot be coded together with E71.540?: E71.540 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above E71.540 (E71.5) and apply to it just the same.