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E00.1

E00.1: Congenital iodine-deficiency syndrome, myxedematous type

Billable / specific codeICD-10-CM

E00.1 is a billable, specific ICD-10-CM code for congenital iodine-deficiency syndrome, myxedematous type. It is valid for submission on a claim.

Check E00.1 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Endemic hypothyroid cretinism
  • Endemic cretinism, myxedematous type

Excludes1 inherited from the categories above E00.1

A category’s note binds every code beneath it.

Written on E00: Congenital iodine-deficiency syndrome

  • subclinical iodine-deficiency hypothyroidism (E02)

Other codes that can never be billed with E00.1

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • E01Iodine-deficiency related thyroid disorders and allied conditions

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

E00.1 is named in 2 Medicare coverage policies: 2 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A57326Billing and Coding: Electrocardiograms
  • A57361Billing and Coding: Monitored Anesthesia Care

Alphabetic index entries that lead here

  • Myxedema›congenital
  • Cretin, cretinism›type›hypothyroid
  • Cretin, cretinism›type›myxedematous
  • Syndrome›iodine-deficiency, congenital›type›myxedematous

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under E00

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.