D70.0 — Congenital agranulocytosis
D70.0 is a billable, specific ICD-10-CM code for congenital agranulocytosis. It is valid for submission on a claim.
Inclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Congenital neutropenia
- Infantile genetic agranulocytosis
- Kostmann's disease
Other codes that can never be billed with D70.0
These codes carry an Excludes1 note pointing at D70.0. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading D70.0 alone.
- P61.5Transient neonatal neutropenia
Risk adjustment
D70.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:
- HCC 115 Specified Immunodeficiencies and White Blood Cell Disorders0.565 RAF
Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.
Medicare coverage
D70.0 is named in 13 Medicare coverage policies — 13 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.
- A55717Billing and Coding: Lab: Flow Cytometry
- A56464Billing and Coding: Flow Cytometry
- A56748Billing and Coding: White Cell Colony Stimulating Factors
- A57689Billing and Coding: Lab: Flow Cytometry
How D70.0 is indexed
Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to D70.0.
- Agranulocytosis›congenital
- Aleukia›congenital
- Disease, diseased›Kostmann's(infantile genetic agranulocytosis)
- Leukopenia›congenital
- Leukopenia›cyclic
- Leukopenia›familial
- Leukopenia›infantile genetic
- Leukopenia›periodic
- Neutropenia, neutropenic›congenital(primary)
- Syndrome›Kostmann's
Related codes at this level
Codes that share D70. If D70.0 is not quite right, the correct code is usually one of these.
Questions about D70.0
- Is D70.0 a billable ICD-10-CM code?
- Yes. D70.0 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
- Where does D70.0 sit in the tabular list?
- Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), in the block Other disorders of blood and blood-forming organs (D70-D77).