MCMedicalCodingSoftware
D70.0

D70.0: Congenital agranulocytosis

Billable / specific codeICD-10-CM

D70.0 is a billable, specific ICD-10-CM code for congenital agranulocytosis. It is valid for submission on a claim.

Check D70.0 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Congenital neutropenia
  • Infantile genetic agranulocytosis
  • Kostmann's disease

Excludes1 inherited from the categories above D70.0

A category’s note binds every code beneath it.

Written on D70: Neutropenia

  • neutropenic splenomegaly (D73.81)
  • transient neonatal neutropenia (P61.5)

Other codes that can never be billed with D70.0

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • P61.5Transient neonatal neutropenia

Risk adjustment

D70.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 115 Specified Immunodeficiencies and White Blood Cell Disorders0.565 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

D70.0 is named in 9 Medicare coverage policies: 9 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A55717Billing and Coding: Lab: Flow Cytometry
  • A56464Billing and Coding: Flow Cytometry
  • A56748Billing and Coding: White Cell Colony Stimulating Factors
  • A57689Billing and Coding: Lab: Flow Cytometry

Alphabetic index entries that lead here

  • Agranulocytosis›congenital
  • Aleukia›congenital
  • Disease, diseased›Kostmann's(infantile genetic agranulocytosis)
  • Leukopenia›congenital
  • Leukopenia›cyclic
  • Leukopenia›familial
  • Leukopenia›infantile genetic
  • Leukopenia›periodic
  • Neutropenia, neutropenic›congenital(primary)
  • Syndrome›Kostmann's

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under D70

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.