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D68.01

D68.01: Von Willebrand disease, type 1

Billable / specific codeICD-10-CM

D68.01 is a billable, specific ICD-10-CM code for von willebrand disease, type 1. It is valid for submission on a claim.

Check D68.01 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Partial quantitative deficiency of von Willebrand factor
  • Type 1C von Willebrand disease

Excludes1 inherited from the categories above D68.01

A category’s note binds every code beneath it.

Written on D68.0: Von Willebrand disease

  • capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)

Written on D68: Other coagulation defects

  • abnormal coagulation profile NOS (R79.1)

Excludes2 inherited from the categories above D68.01

Not part of this code, but both may be coded when both are present.

Written on D68: Other coagulation defects

  • coagulation defects complicating abortion or ectopic or molar pregnancy (O00-O07, O08.1)
  • coagulation defects complicating pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)

Other codes that can never be billed with D68.01

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • R79.1Abnormal coagulation profile

Risk adjustment

D68.01 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 112 Immune Thrombocytopenia and Specified Coagulation Defects and Hemorrhagic Conditions0.450 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

D68.01 is named in 3 Medicare coverage policies: 3 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A56065Billing and Coding: Guidance for Anti-Inhibitor Coagulant Complex (AICC) National Coverage Determination (NCD) 110.3
  • A57954Billing and Coding: Routine Foot Care
  • A59105Billing and Coding: Off-Label Use of Intravenous Immune Globulin (IVIG)

Alphabetic index entries that lead here

  • Deficiency, deficient›von Willebrand factor›partial quantitative
  • Disease, diseased›von Willebrand›type 1
  • Disease, diseased›von Willebrand›type 1C

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under D68.0

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.