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D61.02

D61.02Shwachman-Diamond syndrome

Billable / specific codeICD-10-CM

D61.02 is a billable, specific ICD-10-CM code for shwachman-diamond syndrome. It is valid for submission on a claim.

Use additional code

Add a secondary code to capture the detail described below.

  • code, if applicable, for genetic susceptibility to other malignant neoplasm (Z15.09)

Code also

Both codes may be needed to describe the encounter fully. Sequencing depends on the reason for the visit.

  • , if applicable, associated conditions such as:
  • acute myeloblastic leukemia (C92.0-)
  • exocrine pancreatic insufficiency (K86.81)
  • myelodysplastic syndrome (D46.-)

Risk adjustment

D61.02 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 109 Acquired Hemolytic, Aplastic, and Sideroblastic Anemias1.144 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

D61.02 is named in 6 Medicare coverage policies 6 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A55717Billing and Coding: Lab: Flow Cytometry
  • A56718Billing and Coding: Intravenous Immunoglobulin (IVIG)
  • A57110Billing and Coding: MolDX: Blood Product Molecular Antigen Typing
  • A57124Billing and Coding: MolDX: Blood Product Molecular Antigen Typing

How D61.02 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to D61.02.

  • SyndromeSchwachman(-Diamond)
  • SyndromeShwachman(-Diamond)

Related codes at this level

Codes that share D61.0. If D61.02 is not quite right, the correct code is usually one of these.

Questions about D61.02

Is D61.02 a billable ICD-10-CM code?
Yes. D61.02 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does D61.02 sit in the tabular list?
Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89), in the block Aplastic and other anemias and other bone marrow failure syndromes (D60-D64).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.