MCMedicalCodingSoftware
Q99.1

Q99.1: 46, XX true hermaphrodite

Billable / specific codeICD-10-CMPOA exempt

Q99.1 is a billable, specific ICD-10-CM code for 46, xx true hermaphrodite. It is valid for submission on a claim.

Check Q99.1 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • 46, XX with streak gonads
  • 46, XY with streak gonads
  • Pure gonadal dysgenesis

Other codes that can never be billed with Q99.1

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • Q56Indeterminate sex and pseudohermaphroditism
  • R62Lack of expected normal physiological development in childhood and adults
  • E28.3Primary ovarian failure

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Alphabetic index entries that lead here

  • Swyer syndrome
  • Hermaphrodite, hermaphroditism›46,XX with streak gonads
  • Hermaphrodite, hermaphroditism›46,XY with streak gonads
  • Syndrome›Swyer
  • Dysgenesis›gonadal›pure
  • Karyotype›46,XX›hermaphrodite(true)
  • Karyotype›46,XY›hermaphrodite(true)
  • Anomaly, anomalous›chromosomes, chromosomal›sex›gonadal dysgenesis(pure)

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under Q99

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.