Q89.81
Q89.81: Kabuki syndrome
Billable / specific codeICD-10-CMPOA exempt
Q89.81 is a billable, specific ICD-10-CM code for kabuki syndrome. It is valid for submission on a claim.
Check Q89.81 with the rest of the claim: free scrubberInclusion terms
Alternative wordings a physician may use in the chart for this same code.
- Kabuki syndrome, type 1, due to KMT2D mutation
- Kabuki syndrome, type 2, due to KDM6A mutation
- Niikawa-Kuroki syndrome
Risk adjustment
No CMS-HCC V28 category: this code does not change a RAF score.
Medicare coverage
Q89.81 is named in 4 Medicare coverage policies: 4 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.
- A56726Billing and Coding: Ophthalmology: Posterior Segment Imaging (Extended Ophthalmoscopy and Fundus Photography)
- A56767Billing and Coding: Heavy Metal Testing
- A56781Billing and Coding: Transthoracic Echocardiography (TTE)
- A57071Billing and Coding: Ophthalmology: Posterior Segment Imaging (Extended Ophthalmoscopy and Fundus Photography)
Alphabetic index entries that lead here
- Syndrome›Kabuki(type 1, due to KMT2D mutation) (type 2, due to KDM6A mutation)
- Syndrome›Niikawa-Kuroki
Code history
- addedFY2024-FY2027
Kabuki syndrome