Is Q80.4 a billable ICD-10-CM code?

Yes. Q80.4 is a billable, specific ICD-10-CM code and is valid for submission on a claim.

Where does Q80.4 sit in the tabular list?

Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0), in the block Other congenital malformations (Q80-Q89).

What cannot be coded together with Q80.4?

Q80.4 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above Q80.4 (Q80) and apply to it just the same.

Q80.4

Q80.4 — Harlequin fetus

Billable / specific codeICD-10-CMPOA exempt

Q80.4 is a billable, specific ICD-10-CM code for harlequin fetus. It is valid for submission on a claim.

Excludes1 inherited from the categories above Q80.4

These are not written on Q80.4, but they bind it: a note on a category applies to every code beneath it. Billing Q80.4 with anything listed here is a denial.

Written on Q80 — Congenital ichthyosis

Refsum's disease (G60.1)

Other codes that can never be billed with Q80.4

These codes carry an Excludes1 note pointing at Q80.4. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading Q80.4 alone.

L85.0Acquired ichthyosis

Risk adjustment

Q80.4 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

How Q80.4 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to Q80.4.

Harlequin(newborn)
Ichthyosis›fetalis

Code history

Q80.4 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.

Related codes at this level

Codes that share Q80. If Q80.4 is not quite right, the correct code is usually one of these.

Questions about Q80.4

Is Q80.4 a billable ICD-10-CM code?: Yes. Q80.4 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does Q80.4 sit in the tabular list?: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0), in the block Other congenital malformations (Q80-Q89).
What cannot be coded together with Q80.4?: Q80.4 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above Q80.4 (Q80) and apply to it just the same.