MCMedicalCodingSoftware
Q40.0

Q40.0: Congenital hypertrophic pyloric stenosis

Billable / specific codeICD-10-CMPOA exempt

Q40.0 is a billable, specific ICD-10-CM code for congenital hypertrophic pyloric stenosis. It is valid for submission on a claim.

Check Q40.0 with the rest of the claim: free scrubber

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Congenital constriction
  • Congenital hypertrophy
  • Congenital spasm
  • Congenital stenosis
  • Congenital stricture

Other codes that can never be billed with Q40.0

Their own Excludes1 notes name this code, so the conflict is not listed above.

  • K31.1Adult hypertrophic pyloric stenosis
  • K31.3Pylorospasm, not elsewhere classified
  • K31.BHypertrophic pyloric stenosis, in childhood

Risk adjustment

Q40.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 78 Intestinal Obstruction/Perforation0.326 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score. Look up the whole chart to see which of its HCCs the hierarchy would zero.

Medicare coverage

Q40.0 is named in 1 Medicare coverage policy: 1 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A57063Billing and Coding: Diagnostic and Therapeutic Esophagogastroduodenoscopy

Alphabetic index entries that lead here

  • Achalasia›pylorus
  • Pylorospasm NEC›congenital
  • Pylorospasm NEC›newborn
  • Constriction›pylorus›congenital
  • Constriction›pylorus›newborn
  • Hypertrophy, hypertrophic›pylorus›congenital
  • Obstruction, obstructed, obstructive›pylorus›congenital
  • Spasm, spastic, spasticity›pylorus NEC›congenital
  • Stenosis, stenotic›pylorus›congenital
  • Stricture›pylorus›congenital

Code history

Unchanged in every release from FY2024 to FY2027.

Other codes under Q40

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.