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Q03.0

Q03.0Malformations of aqueduct of Sylvius

Billable / specific codeICD-10-CMPOA exempt

Q03.0 is a billable, specific ICD-10-CM code for malformations of aqueduct of sylvius. It is valid for submission on a claim.

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Anomaly of aqueduct of Sylvius
  • Obstruction of aqueduct of Sylvius, congenital
  • Stenosis of aqueduct of Sylvius

Excludes1 inherited from the categories above Q03.0

These are not written on Q03.0, but they bind it: a note on a category applies to every code beneath it. Billing Q03.0 with anything listed here is a denial.

Written on Q03 Congenital hydrocephalus

  • Arnold-Chiari syndrome, type II (Q07.0-)
  • acquired hydrocephalus (G91.-)
  • hydrocephalus due to congenital toxoplasmosis (P37.1)
  • hydrocephalus with spina bifida (Q05.0-Q05.4)

Other codes that can never be billed with Q03.0

These codes carry an Excludes1 note pointing at Q03.0. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading Q03.0 alone.

  • G91Hydrocephalus
  • Q75Other congenital malformations of skull and face bones

Risk adjustment

Q03.0 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 182 Spinal Cord Disorders/Injuries0.478 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

Q03.0 is named in 3 Medicare coverage policies 3 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A54111Billing and Coding: Speech Language Pathology (SLP) Services: Communication Disorders
  • A56612Billing and Coding: CT of the Head
  • A57204Billing and Coding: MRI and CT Scans of the Head and Neck

How Q03.0 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to Q03.0.

  • Anomaly, anomalousaqueduct of Sylvius
  • Atresia, atreticaqueduct of Sylvius
  • Hydrocephalusaqueduct Sylvius stricture
  • Septum, septateaqueduct of Sylvius
  • Stenosis, stenoticaqueduct of Sylvius(congenital)
  • Strictureaqueduct of Sylvius(congenital)
  • Obstruction, obstructed, obstructiveaqueduct of Sylviuscongenital
  • Occlusion, occludedaqueduct of Sylviuscongenital

Code history

Q03.0 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.

Related codes at this level

Codes that share Q03. If Q03.0 is not quite right, the correct code is usually one of these.

Questions about Q03.0

Is Q03.0 a billable ICD-10-CM code?
Yes. Q03.0 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does Q03.0 sit in the tabular list?
Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0), in the block Congenital malformations of the nervous system (Q00-Q07).
What cannot be coded together with Q03.0?
Q03.0 carries Excludes1 notes, which means the conditions they list can never be coded together with it on the same encounter. Some are written on the categories above Q03.0 (Q03) and apply to it just the same.
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.