MCMCB Pro
N01

N01Rapidly progressive nephritic syndrome

Non-billable headerICD-10-CM

N01 is a non-billable header ICD-10-CM code for rapidly progressive nephritic syndrome. It cannot be billed on its own: choose one of the more specific child codes below.

Excludes1 — never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • nephritic syndrome NOS (N05.-)

Includes

Conditions this code covers.

  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Other codes that can never be billed with N01

These codes carry an Excludes1 note pointing at N01. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading N01 alone.

  • N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
  • N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritis

Risk adjustment

N01 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Code to one of these instead N01

11 child codes. Green means billable.

Questions about N01

Is N01 a billable ICD-10-CM code?
No. N01 is a non-billable header code. Code to a higher level of specificity using one of its child codes.
Where does N01 sit in the tabular list?
Diseases of the genitourinary system (N00-N99), in the block Glomerular diseases (N00-N08).
What cannot be coded together with N01?
N01 carries an Excludes1 note, which means the conditions it lists can never be coded together with it on the same encounter.
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.