N01
N01: Rapidly progressive nephritic syndrome
Non-billable headerICD-10-CM
N01 is a non-billable header ICD-10-CM code for rapidly progressive nephritic syndrome. It cannot be billed on its own: choose one of the more specific child codes below.
Excludes1: never code together
These conditions cannot occur together. Billing both on the same encounter is a denial.
- nephritic syndrome NOS (N05.-)
Includes
Conditions this code covers.
- rapidly progressive glomerular disease
- rapidly progressive glomerulonephritis
- rapidly progressive nephritis
Other codes that can never be billed with N01
Their own Excludes1 notes name this code, so the conflict is not listed above.
Risk adjustment
No CMS-HCC V28 category: this code does not change a RAF score.
Code history
Unchanged in every release from FY2024 to FY2027.
Code to one of these instead N01
11 child codes. Green means billable.
- N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
- N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
- N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
- N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
- N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
- N01.6Rapidly progressive nephritic syndrome with dense deposit disease
- N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
- N01.8Rapidly progressive nephritic syndrome with other morphologic changes
- N01.9Rapidly progressive nephritic syndrome with unspecified morphologic changes
- N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritis