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K00.5

K00.5Hereditary disturbances in tooth structure, not elsewhere classified

Billable / specific codeICD-10-CM

K00.5 is a billable, specific ICD-10-CM code for hereditary disturbances in tooth structure, not elsewhere classified. It is valid for submission on a claim.

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Amelogenesis imperfecta
  • Dentinogenesis imperfecta
  • Odontogenesis imperfecta
  • Dentinal dysplasia
  • Shell teeth

Excludes2 inherited from the categories above K00.5

Also inherited, and the opposite of Excludes1: these conditions are not part of K00.5, but a patient can have both, so you may code both.

Written on K00 Disorders of tooth development and eruption

  • embedded and impacted teeth (K01.-)

Risk adjustment

K00.5 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

How K00.5 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to K00.5.

  • Amelogenesis imperfecta
  • Brown enamel of teeth(hereditary)
  • Dentinogenesis imperfecta
  • Odontogenesis imperfecta
  • Opalescent dentin(hereditary)
  • Shell teeth
  • Defect, defectivedentin(hereditary)
  • Dentinopalescent
  • Dysplasiadentinal
  • Disturbancetoothstructure, hereditary NEC

Code history

K00.5 has not changed since FY2024 — no addition, revision or deletion across the three most recent ICD-10-CM releases.

Related codes at this level

Codes that share K00. If K00.5 is not quite right, the correct code is usually one of these.

Questions about K00.5

Is K00.5 a billable ICD-10-CM code?
Yes. K00.5 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does K00.5 sit in the tabular list?
Diseases of the digestive system (K00-K95), in the block Diseases of oral cavity and salivary glands (K00-K14).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.