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I42.81

I42.81: Arrhythmogenic cardiomyopathy

Billable / specific codeICD-10-CM

I42.81 is a billable, specific ICD-10-CM code for arrhythmogenic cardiomyopathy. It is valid for submission on a claim.

Check I42.81 with the rest of the claim: free scrubber

Excludes2 inherited from the categories above I42.81

Not part of this code, but both may be coded when both are present.

Written on I42: Cardiomyopathy

  • ischemic cardiomyopathy (I25.5)
  • peripartum cardiomyopathy (O90.3)
  • ventricular hypertrophy (I51.7)

Risk adjustment

No CMS-HCC V28 category: this code does not change a RAF score.

Medicare coverage

I42.81 is named in 33 Medicare coverage policies: 33 listing it as supporting medical necessity. Which one applies depends on your Medicare contractor.

  • A52458Automatic External Defibrillators - Policy Article
  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A52868Billing and Coding: Transesophageal Echocardiography (TEE)
  • A56391Billing and Coding: Implantable Automatic Defibrillators

Alphabetic index entries that lead here

  • Cardiomyopathy›arrhythmogenic
  • Dysplasia›arrhythmogenic right ventricular
  • Dysplasia›right ventricular, arrhythmogenic
  • Dysplasia›ventricular, arrhythmogenic(biventricular) (left) (right)
  • Cardiomyopathy›arrhythmogenic›biventricular
  • Cardiomyopathy›arrhythmogenic›ventricular(left) (right)

Code history

  • addedFY2024-FY2027

    Arrhythmogenic cardiomyopathy

Other codes under I42.8

ICD-10-CMFY2027· effective October 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release: see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.